CASE REPORT
Steroid Secreting Dedifferentiated Liposarcoma: A Unique Presentation
Steroid Salgılayan Dediferansiye Liposarkom: Özgün Bir Sunum
Received Date : 27 Aug 2019
Accepted Date : 04 Jan 2020
Available Online : 16 Jan 2020
Lucas Ribeiro dos SANTOS, Márcio Luis DUARTE*, José Viana Lima JÚNİOR**
Clinic of Endocrinology and Metabology at Medical Sciences Faculty of Santos, São Paulo, Brazil
*Radiologist of Webimagem. Avenida Marquês de São Vicente, 446, São Paulo – SP., Brazil
**Clinic of Endocrinology and metabology at Medical Sciences Faculty of Santa Casa de Misericórdia de São Paulo, São Paulo, Brazil
Doi: 10.25179/tjem.2019-71188 - Makale Dili: EN
Turk J Endocrinol Metab 2020;24:101-104
ABSTRACT
Adrenal tumors are cancerous or non-cancerous growths on
the adrenal glands. It can originate from the cortex or the
medulla, and may or may not have the capacity to secrete
hormones. We report a case of a 76-year-old man who was
diagnosed with an adrenal mass during abdominal pain investigation.
His biochemical profile and magnetic resonance
images are compatible with adrenocortical carcinoma, while
the pathology reports are compatible with liposarcoma. So
far, to the best of our knowledge, there is no report on steroid-
secreting tumors.
Keywords: Adrenal cancer; dedifferentiated liposarcoma; Cushing syndrome
ÖZET
Adrenal tümörler, adrenal bezlerdeki kanseröz veya nonkanseröz
büyümelerdir. Korteks veya medulladan kaynaklanabilirler
ve hormon salgılama kapasitesine sahip olabilir
veya olmayabilirler. Burada, karın ağrısı muayenesi sırasında
adrenal kitle tanısı konan 76 yaşında bir erkek olgu sunduk.
Olgunun biyokimyasal profili ve manyetik rezonans görüntüleri
adrenokortikal karsinom ile patoloji raporları liposarkom
ile uyumlu idi. Bildiğimiz kadarıyla, şimdiye kadar
steroid salgılayan tümörler hakkında bir olgu sunumu bulunmamaktadır.
Anahtar Kelimeler: Adrenal kanser; dediferansiye liposarkom; Cushing sendromu
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