CASE REPORT
Giant Malignant Pheochromocytoma: A Unique Case Report from Turkey
Dev Malign Feokromositoma Vakası
Received Date : 22 Jun 2020
Accepted Date : 25 Sep 2020
Available Online : 16 Oct 2020
Damla TÜFEKÇİ, Yasemin E. GÜNAY, Ahmet Suat DEMİR, İrfan NUHOĞLU, Hülya COŞKUN, Özge ÜÇÜNCÜ, Mustafa KOÇAK
Department of Endocrinology and Metabolism, Karadeniz Technical University Faculty of Medicine, Trabzon, TURKEY
Doi: 10.25179/tjem.2020-77474 - Makale Dili: EN
Turk J Endocrinol Metab. 2020;24:356-360
ABSTRACT
Catecholamine-secreting tumors are rare neoplasms that
occur in less than 0.2% of hypertensive patients. While pheochromocytomas
are rare neoplasms in the adrenal gland,
giant pheochromocytomas are much less common. In this
report, we present the case of a 38-year-old man who had
a 29x18x12 cm giant malignant pheochromocytoma. During
an examination for hematuria, a large mass was detected
incidentally in the right adrenal gland of the patient.
This mass was diagnosed as pheochromocytoma and proved
to be one of the largest pheochromocytomas reported so
far; hence, its notification has been considered significant
for the medical and research professionals across the world.
Keywords: Adrenal incidentaloma; pheochromocytoma; hematuria; hypertension, malignant; chromaffin cells
ÖZET
Katekolamin salgılayan tümörler, hipertansiyonu olan hastaların
yüzde 0,2’sinden daha azında görülen nadir neoplazilerdir.
Feokromositomalar adrenal bezde görülen nadir
neoplazilerken, dev feokromositomalar çok daha nadir görülmektedir.
Bu vaka bildiriminde 38 yaşında 29x18x12 cm
boyutlarında dev malign feokromositoma tespit edilen bir
erkek hasta tanımlanmıştır. Hasta hematüri nedeni ile tetkik
edilirken sağ adrenal bezinde insidental olarak kitle tespit
edilmiştir. Türkiye’de tanımlanmış en büyük feokromositomalardan
biri olarak bildiriminin önemli olabileceği düşünülmüştür.
Anahtar Kelimeler: Adrenal insidentalom; feokromositoma; hematüri; hipertansiyon, malign; kromafin hücreler
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