ISSN: 1301-2193 E-ISSN: 1308-9846
  • Turkish Journal of
    Endocrinology and Metabolism
CASE REPORT

Giant Malignant Pheochromocytoma: A Unique Case Report from Turkey
Dev Malign Feokromositoma Vakası
Received Date : 22 Jun 2020
Accepted Date : 25 Sep 2020
Available Online : 16 Oct 2020
Doi: 10.25179/tjem.2020-77474 - Makale Dili: EN
Turk J Endocrinol Metab. 2020;24:356-360
Bu makale, CC BY-NC-SA altında lisanslanmış açık erişim bir makaledir.
ABSTRACT
Catecholamine-secreting tumors are rare neoplasms that occur in less than 0.2% of hypertensive patients. While pheochromocytomas are rare neoplasms in the adrenal gland, giant pheochromocytomas are much less common. In this report, we present the case of a 38-year-old man who had a 29x18x12 cm giant malignant pheochromocytoma. During an examination for hematuria, a large mass was detected incidentally in the right adrenal gland of the patient. This mass was diagnosed as pheochromocytoma and proved to be one of the largest pheochromocytomas reported so far; hence, its notification has been considered significant for the medical and research professionals across the world.
ÖZET
Katekolamin salgılayan tümörler, hipertansiyonu olan hastaların yüzde 0,2’sinden daha azında görülen nadir neoplazilerdir. Feokromositomalar adrenal bezde görülen nadir neoplazilerken, dev feokromositomalar çok daha nadir görülmektedir. Bu vaka bildiriminde 38 yaşında 29x18x12 cm boyutlarında dev malign feokromositoma tespit edilen bir erkek hasta tanımlanmıştır. Hasta hematüri nedeni ile tetkik edilirken sağ adrenal bezinde insidental olarak kitle tespit edilmiştir. Türkiye’de tanımlanmış en büyük feokromositomalardan biri olarak bildiriminin önemli olabileceği düşünülmüştür.
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